Product: | 3-Hydroxyisovaleric Acid | ||||||||
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Catalog Number: | 5178 | ||||||||
CAS Number: | 625-08-1 | ||||||||
Synonyms: |
β-Hydroxy β-methylbutyric acid; HMB |
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Pricing: |
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Chemical Purity: | 96% | ||||||||
Molecular Weight: | 118.13 | ||||||||
Structure: | |||||||||
Category: | Reference Standards for Inborn Errors | ||||||||
Literature References: |
Mock, D.M., Henrich, C.L., Carnell, N., Mock, N.I., Indicators of marginal biotin deficiency and repletion in humans: validation of 3-hydroxyisovaleric acid excretion and a leucine challenge. Am J Clin Nutr, 2002, 76(5):1061-1068. |
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MSDS: | |||||||||
Applications: | Metabolite of leucine excreted in the urine. Elevated levels are a marker for Dihydrolipoamide dehydrogenase deficiency among other disorders. Also elevated levels are seen in smokers. |