Product: | N-Isovaleroylglycine | ||||
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Catalog Number: | 5211 | ||||
CAS Number: | 16284-60-9 | ||||
Synonyms: |
N-4-Methylbutyrylglycine; N-Isovalerylglycine; Isovalerylaminoacetic acid |
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Pricing: |
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Formula: | C7H13NO3 | ||||
Chemical Purity: | >97.0% | ||||
Molecular Weight: | 159.19 | ||||
Structure: | |||||
Appearance: | White solid | ||||
Category: | Reference Standards for Inborn Errors | ||||
Stability: | Stable under recommended storage conditions. | ||||
Storage: |
Store at room temperature. Adequate ventilation |
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Transportation: |
Non-hazardous for transport |
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Literature References: |
Lin, H.-M., Helsby, N.A., Rowan, D.D., Ferguson, L.R., Using metabolomic analysis to understand inflammatory bowel diseases. Inflammatory Bowel Diseases, 2011, 17(4):1021-1029. |
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MSDS: | |||||
Applications: | Found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabolism. Used to diagnose many organic acidemias and mitochondrial fatty acid beta-oxidation defects. |