Product: | 3-Phenylpropionyl glycine | ||||
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Catalog Number: | 5220 | ||||
CAS Number: | 56613-60-6 | ||||
Pricing: |
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Molecular Weight: | 207.22 | ||||
Structure: | |||||
Category: | Reference Standards for Inborn Errors | ||||
Literature References: |
Rinaldo P, O'Shea JJ, Coates PM, Hale DE, Stanley CA, Tanaka K: Medium-chain acyl-CoA dehydrogenase deficiency. Diagnosis by stable-isotope dilution measurement of urinary n-hexanoylglycine and 3-phenylpropionylglycine. N Engl J Med., 1988, 319(20):1308-13. |
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MSDS: | |||||
Applications: | A metabolite of fatty acids. Used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Levels in the urine are used to diagnose deficiency of medium-chain acyl-CoA dehydrogenase. |