Inquire About a Product| Product: | 2-Methylbutyroyl carnitine | ||||
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| Catalog Number: | 5242 | ||||
| CAS Number: | 31023-25-3 | ||||
| Synonyms: | (2-methylbutyryl)carnitine; 2-Methylbutyroylcarnitine; L-2-methylbutyrate (3-carboxy-2-hydroxypropyl)trimethyl-hydroxide Ammonium inner | ||||
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| Formula: | C12H23NO4 | ||||
| Chemical Purity: | 99.9% | ||||
| Molecular Weight: | 281.77 | ||||
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| Category: | Biochemicals and Reagents | ||||
| Literature References: |
Farook, V.S., et al., Metabolites as novel biomarkers for childhood obesity-related traits in Mexican-American children. Pediatric Obesity, 2015 Aug., 10(4):320-327. |
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| Applications: |
Usually not detected in normal individuals, the elevation of 2-methylbutyrylcarnitine suggests a deficiency of a dehydrogenase specific for isobutyryl-CoA, important in the differential diagnosis of Branched Chain Organic Acidurias by Analysis of Urinary Organic Acids and Acylcarnitines in Plasma or Dried Blood Spots (The Metabolic and Molecular Bases of Inherited Disease, Chapter 93) |